Catecholaminergic polymorphic ventricular tachycardia
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Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a condition characterised by an abnormal heart rhythm (arrhythmia). As the heart rate increases in response to physical activity or emotional stress, it can trigger an abnormally fast heartbeat called ventricular tachycardia. Episodes of ventricular tachycardia can cause light-headedness, dizziness, and fainting (syncope). In people with CPVT, these episodes typically begin in childhood.
Beschreibung
Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a condition characterised by an abnormal heart rhythm (arrhythmia). As the heart rate increases in response to physical activity or emotional stress, it can trigger an abnormally fast heartbeat called ventricular tachycardia. Episodes of ventricular tachycardia can cause light-headedness, dizziness, and fainting (syncope). In people with CPVT, these episodes typically begin in childhood.
If CPVT is not recognized and treated, an episode of ventricular tachycardia may cause the heart to stop beating (cardiac arrest), leading to sudden death. Researchers suspect that CPVT may be a significant cause of sudden death in children and young adults without recognized heart abnormalities.
Inheritance patterns
The source lists the following possible inheritance patterns: Autosomal dominant; Autosomal recessive. More than one pattern can apply in different cases.
Related genes
Other names
Bidirectional tachycardia induced by catecholamines
Catecholamine-induced polymorphic ventricular tachycardia
CPVT
Familial polymorphic ventricular tachycardia
FPVT
Related patient information and medicines
Patient information leaflet
Unregelmäßige Herzrhythmen
An arrhythmia is an abnormal rate and/or rhythm of the heartbeat due to some problem with the electrical conducting system of the heart. What is an arrhythmia. An arrhythmia is an abnormal rate and/or rhythm of the heartbeat. Atr... The atria contract at about 300 bpm but the ventricles are unable to beat that quickly and so beat at between 75 and.
Patient information leaflet
Wolff-Parkinson-White-Syndrom
Wolff-Parkinson-White-Syndrom is not common but can cause a fast Herz rate or other heart rhythm abnormalities from time to time. Treatment can be given for the fast heart rate and also to prevent any further episodes. In Wolff-Parkinson-White (WPW) Syndrom there is an extra connection (an accessory pathway) between the atria and ventricles..
Patient information leaflet
Herzklopfen
Herzklopfen sind the sensation of dein heart beating and are common. Most cases are harmless. They usually only last for a short time and can be accompanied by other symptoms such as breathlessness, dizziness, chest tightness and a feeling of anxiety. Palpitations that are severe or don't settle quickly may need urgent medical attention. The.
Patient information leaflet
Herzkrankheit
The heart is a muscle pump located in the chest, which pumps Blut around the body. It keeps pumping from a few weeks after conception until we die. There are a number of different conditions that can affect how the heart works. What is heart disease. There are many different conditions which can affect the heart, including those which affect the.
Patient information leaflet
Borholm-Krankheit
Bornholm disease is an illness which causes flu-like symptoms, together with pain in the chest or tummy (abdomen). It usually lasts for only a few days. Complications rarely occur. Most people make a full recovery within days or weeks. However, the following complications have been seen in a few cases: Heart problems - Entzündung around the.
Patient information leaflet
Betablocker
Betablocker sind Medikamenten that are used to treat a variety of conditions. Their full correct name is beta-adrenoceptor blocking medicines (or beta-adrenergic blocking agents), but they are commonly just called beta-blockers. How do beta-blockers work. Lower your blood pressure if you have high blood pressure. Treat postural tachycardia syndrome.
Weiterführende Lektüre und Referenzen
- Catecholaminergic polymorphic ventricular tachycardia; MedlinePlus, National Library of Medicine.
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18. Aug 2020 | Neueste Version
1. Juli 2020 | Ursprünglich veröffentlicht
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